(Click image for full size)Clinical triad of port wine nevus (hemangioma), lower extremity swelling and varicose veins. A congenital malformation of vascular and lymphatic structures usually in the lower extremities. Pateints develope lower extremity enlargement. May develope large lymphangiomas and hemangiomas.
Image A and D: Coronal and axial T2 fat supressed MRI of lower extremities in a 14m old male infant. Note the large perineal lymphatic mass extending upinto the pelvis. Also near the knees there are other vascular / lymphatic malformations.
Image B: Image fusion of contrast MRA with conventional T2 MRI in volume rendering. You can now see the full exrtent of the vascular / lymphatic malformations in 3D with ther relationship to the arteries. Note the limited visualization of lower extremity arteries in the left calf. Patients with KT syndrome can have arterial abnormalities including atresias in the lower extremities.
Image D: Fusion of MR venogram with T2 coronal images in volume rendering. Tee entire deep venous system has been replaced by extensive collaterals. The large lateral venous channels in the thighs are called Trenaunay veins.
THANK YOU for providing Klippel-Trenaunay images. I am a KT sufferer and had to build a website (http://klippel-trenaunay.webs.com)to educate my local doctor and emergency room. I have added a link to your blog post, this is a valuable resource - you are appreciated!
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